Congenital Pulmonary Airway Malformation Type 2: A Case Report with Review of the Literature

dc.authoridÖzdemir, Çiğdem/0000-0001-8500-0744
dc.authoridYALCIN, OMER TARIK/0000-0001-5626-1881;
dc.authorwosidÖzdemir, Çiğdem/HNQ-6804-2023
dc.authorwosidYALCIN, OMER TARIK/B-4744-2018
dc.authorwosidOzyilmaz, Filiz/A-4865-2016
dc.contributor.authorTastekin, Ebru
dc.contributor.authorUsta, Ufuk
dc.contributor.authorKaynar, Aysegul
dc.contributor.authorOzdemir, Cigdem
dc.contributor.authorYalcin, Omer
dc.contributor.authorOzyilmaz, Filiz
dc.contributor.authorKutlu, Ali Kemal
dc.date.accessioned2024-06-12T10:59:06Z
dc.date.available2024-06-12T10:59:06Z
dc.date.issued2016
dc.departmentTrakya Üniversitesien_US
dc.description.abstractA congenital pulmonary airway malformation is a rare disorder of the pulmonary airway and a hamartomatous mass of disorganized lung tissues with various degrees of cystic change. A 20-year-old pregnant woman who did not have previous clinical follow-up during her pregnancy visited the gynecology department for her first check on the 19th week of gestation. The sonogram, showed severe hydrops fetalis. Laboratory findings were consistent with non-immune hydrops fetalis. Medical abortion was performed and the fetus was sent to our department for a complete fetal autopsy. Macroscopically, whole parts of the fetus had striking oedema. Massive pleural and peritoneal effusions were seen on dissection. The left lung filled the whole thoracic cavity. The heart was displaced to the right and the right lung was compressed. Microscopically, the left lung mass showed dilated bronchiole-like structures (1-20 mm) that were lined with ciliated columnar cells without any intervening mucinous cells. The subepithelial stroma contained thin, interrupted smooth muscle fibers and elastic connective tissue without cartilage plates. Our case is a very good example of non-immune hydrops fetalis associated with congenital pulmonary airway malformation type 2. Prenatal clinical and ultrasonographic follow-ups during pregnancy are very important for early diagnosis of congenital malformations.en_US
dc.identifier.doi10.5146/tjpath.2013.01208
dc.identifier.endpage204en_US
dc.identifier.issn1018-5615
dc.identifier.issn1309-5730
dc.identifier.issue3en_US
dc.identifier.pmid24715554en_US
dc.identifier.scopus2-s2.0-84983372369en_US
dc.identifier.scopusqualityQ3en_US
dc.identifier.startpage200en_US
dc.identifier.urihttps://doi.org/10.5146/tjpath.2013.01208
dc.identifier.urihttps://hdl.handle.net/20.500.14551/20314
dc.identifier.volume32en_US
dc.identifier.wosWOS:000393337600010en_US
dc.identifier.wosqualityN/Aen_US
dc.indekslendigikaynakWeb of Scienceen_US
dc.indekslendigikaynakScopusen_US
dc.indekslendigikaynakPubMeden_US
dc.language.isoenen_US
dc.publisherDe Gruyter Open Ltden_US
dc.relation.ispartofTurkish Journal Of Pathologyen_US
dc.relation.publicationcategoryMakale - Uluslararası Hakemli Dergi - Kurum Öğretim Elemanıen_US
dc.rightsinfo:eu-repo/semantics/openAccessen_US
dc.subjectCystic Adenomatoid Malformation Of Lungen_US
dc.subjectCongenitalen_US
dc.subjectLung Diseasesen_US
dc.subjectHydrops Fetalisen_US
dc.subjectCystic Adenomatoid Malformationen_US
dc.subjectLungen_US
dc.subjectManagementen_US
dc.titleCongenital Pulmonary Airway Malformation Type 2: A Case Report with Review of the Literatureen_US
dc.typeReview Articleen_US

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