Successful pregnancy and delivery management in a patient with Bernard Soulier Syndrome
Küçük Resim Yok
Tarih
2023
Dergi Başlığı
Dergi ISSN
Cilt Başlığı
Yayıncı
Sage Publications Ltd
Erişim Hakkı
info:eu-repo/semantics/closedAccess
Özet
Bernard Soulier Syndrome (BSS) is an inherited bleeding disorder characterized by macrothrombocytopenia and absence of ristocetin-induced platelet aggregation. Clinical findings vary from person to person. Most of the patients are diagnosed with muco-cutaneous bleeding such as purpura, epistaxis and gingival bleeding in early childhood. Few pregnant women with BSS are described in the literature. Management of thrombocytopenia during pregnancy and delivery requires a multidisciplinary approach. The family should be warned about the potentially life-threatening bleeding during pregnancy and the delivery and the decision about mode of delivery should be individualised, involving discussion with patient and multidisciplinary team.
Açıklama
Anahtar Kelimeler
Pregnancy, Bernard Soulier Syndrome, Macrothrombocytopenia, Thrombosis
Kaynak
Obstetric Medicine
WoS Q Değeri
N/A
Scopus Q Değeri
Q3
Cilt
16
Sayı
3
